Autosomal Recessive Polycystic Kidney
Section Editor: Dharam M. Ramnani, MD
Virginia Urology, Richmond, VA, USA
Image Description
Autosomal recessive polycystic kidney disease (ARPKD) - Macroscopic Features: Autopsy photo from a case of ARPKD that resulted in perinatal demise. It shows symmetrically enlarged kidneys, urinary bladder, ureters, urachus and umbilicus. The two medial umbilical ligaments (obliterated fetal umbilical arteries) are seen at the top of the image. The kidneys have smooth external surface. See cut section in the next photo.