Autosomal Recessive Polycystic Kidney
Section Editor: Dharam M. Ramnani, MD
Virginia Urology, Richmond, VA, USA
Image Description
Autosomal recessive polycystic kidney disease (ARPKD) - Macroscopic Features: The cut surface shows diffuse replacement of the renal parenchyma by numerous tubular cysts, 1-2 mm in diameter, radiating linearly from the medulla to the cortex, giving kidneys a spongy appearance. The cortico-medullary junction is indistinct. (close-up of the previous photo).